Asociación entre desnutrición y fibrosis quística en pacientes pediátricos del Hospital de Niños Dr. Roberto Gilbert del 2014 al 2022.

Abstract

Introduction: Cystic Fibrosis a disease of hereditary character, multisystemic and chronic, which is characterized by affecting mainly the respiratory system and the digestive system. Malnutrition in Cystic Fibrosis plays a fundamental role in the evolution of the disease and its complications. Methodology: This is an observational, retrospective, cross-sectional, descriptive study carried out at the Dr. Roberto Gilbert Children Hospital by reviewing medical records. This database was used to collect and analyze the reported cases of Cystic Fibrosis during the period of 2014 to 2022, where 82 medical records were obtained that met the criteria. Results: Of the 82 patients in the study, 44 (53.7%) were male and 38 (46.3%) were female. Of the patients, 48.8% were diagnosed between 0 and 2 years of age, 22% between 3 and 5 years of age and 29.3% after 6 years of age. Regarding malnutrition 44 patients suffered from it and 28 were less than 2 years old. 36.6% were severely malnourished, 9.8% were moderately malnourished, 7.3% were mildly malnourished, 28% were normal weight, 7.3% were overweight and 11% were obese. Pancreatic insufficiency was present in 62.7% of patients. Conclusion: Patients diagnosed with cystic fibrosis between 0 and 2 years old are more prone to malnutrition. There is a direct correlation between better nutrition and higher FEV1. Multidisciplinary management is the key to increase the quality of life for patients with this pathology.